hrp0082p3-d1-706 | Diabetes | ESPE2014
Vitaliti Marcello
, Maggio Maria Cristina
, Vitaliti Giuliana
, Grasso Valeria
, Ciofalo Amalia
, Rinaudo Grazia
, Tranchina Elisa
, Costantino Giuseppina
, Corsello Giovanni
, Barbetti Fabrizio
Background: Leprechaunism, also known as Donohue syndrome, is due to a severe congenital insulin-resistance, with prenatal and neonatal growth retardation, typical dysmorphic features, glycaemic dysregulation with hyperinsulinism and hyperandrogenism.Objective and hypotheses: These patients have a poor prognosis with death in the first year of life.Method: We report the case of a newborn (35.4 weeks) with severe fetal growth restri...