hrp0098p3-294 | Late Breaking | ESPE2024

Hepatic glycogenosis in poorly controlled type 1 diabetics: four case reports

Zerguine Halima , Boukhalfa Imène , Bensassia Norhane , Hadef Djohra

Introduction: Mauriac syndrome is a rare condition affecting poorly controlled type 1 diabetics. It results from excessive accumulation of glycogen in the liver following chronic hyperglycaemia. It is manifested by delayed growth and pubertal development, as well as hepatomegaly and hepatic cytolysis. Early detection can improve the prognosis and prevent progression to serious complications. Our aimis to report the diagnostic and evolutionary features of four ...