hrp0098p2-22 | Adrenals and HPA Axis | ESPE2024

Severe Adrenocortical Carcinoma Presentation with Vena Cava Involvement in a 1-Year-Old Boy: A Case Presentation and Management Considerations

Cvetković Dimitrije , Vuković Rade , Milenković Tatjana , Todorović Slađana , Mitrović Katarina , Panić Zarić Sanja , Čehić Maja , Đokić Dragomir , Redžić Danka , Aleksić Dragana , Radeta Ratko , Dattani Mehul , Mushtaq Imran , Jorgensen Mette , Muthialu Nagarajan , Watson Tom , Nguyen Trung

Introduction: Adrenocortical carcinoma (ACC) is a rare malignancy in children, presenting diagnostic and therapeutic challenges. This case report details the presentation, workup, and initial management of a highly aggressive ACC in a young infant.Case Presentation: A 12-month-old boy presented with premature pubarche. Parents also noticed rapid weight gain, increased body hair growth, and penile enlargement. Clinical pi...