hrp0084p1-47 | Diabetes | ESPE2015

Relative Hypoaldosteronism in a Patient with WOLCOTT-Rallison Syndrome

Ucar Ahmet , Aydemir Yusuf , Dogan Ayse , Tuncez Ebru

Background: Wolcott–Rallison syndrome (WRS) is an autosomal recessive, multi-system disorder with early onset diabetes in infancy. It is associated with clinical features that show variability between WRS cases. Clinical data are still scarce.Patient data: A 9 year old girl followed-up due to diabetes and growth failure since 2 months of age from another centre presented with ketoacidosis and multi-organ failure. After resolution of her decompansate...