hrp0094p2-367 | Pituitary, neuroendocrinology and puberty | ESPE2021

Duplication of Pituitary Gland-plus Syndrome presenting with a Transcranial Nasal Dermoid Cyst

Chandwani Manju , Spilioti Diamantina-Xanthi , Chumas Paul , Symth Alistair , Alvi Sabah , Nix Paul , Warren Daniel , Liddington Mark , Russell John , Elliott Mark ,

Duplicated pituitary gland in association with other midline craniofacial anomalies – also described as DPG-plus syndrome – is extremely rare. So far the only described endocrine associations are precocious or delayed puberty. We describe the multifaceted management of a female infant with DPG-plus syndrome. Interestingly, the patient also presented with trans-cranial nasal dermoid cyst and a nasal dimple with protruding hair, which has not been described in previous...